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Case Studies | Anaesthesiology | India | Volume 9 Issue 7, July 2020 | Rating: 6.5 / 10
Anaesthesia Management in Waardenburg Syndrome with Hirschsprungs Disease
Dr. G. D. Sree Mounika | Dr. Y. Murali Prabakar | Dr. M. Sharada | Dr. R. Kondareddy [3] | Dr. C. G. Raghuram [9]
Abstract: Waardenburg syndrome type 4 is a rarely occurring pediatric emergency in association with mega colon and Hirschsprung’s disease. We hereby report a case of type 4 Waardenburg syndrome with Hirschsprung’s disease coming up for an emergency decompressive colostomy. The anaesthetic implications and the multisystem involvement relevant to the syndrome are discussed and presented in this paper.
Keywords: Shah-Waardenburg syndrome, stomach decompression, aspiration pneumonitis, Isolate-P
Edition: Volume 9 Issue 7, July 2020,
Pages: 1874 - 1875