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Case Studies | Paediatrics | India | Volume 9 Issue 3, March 2020 | Rating: 6.6 / 10
A Rare Case Report on Kaposiform Hemangioendothelioma with Kasabach Meritt Syndrome
Dr. Ajay Vaid, Dr. Amar Singh Thakur, Dr. Mohit Bajaj
Abstract: Tufted angioma and kaposiform hemangioendothelioma are rare vascular tumours that typically occurduring infancy or early childhood. Kasabach-Merritt syndrome is characterised by the combination of rapidly growing vascular tumour, life threatening thrombocytopenia, microangiopathic haemolytic anaemia and consumptive coagulopathy [1]. The blood clotting disorder results from platelets and other clotting factors of the blood being used up within the tumor. Here we report a newborn presenting with swelling left side of neck with bluish tinge on day 1 of life.
Keywords: Kasabach-Merritt syndrome KMS, Hemangioma, Thrombocytopenia, Hypofibrinogenemia
Edition: Volume 9 Issue 3, March 2020
Pages: 953 - 955