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Subjective Paper | Medicine | India | Volume 13 Issue 5, May 2024 | Rating: 4.7 / 10
Ebstein's Anomaly Unveiled: Hemodynamic Compromise as the Key Diagnostic Clue - A Case Report
Abstract: Background: Ebstein's anomaly is a rare congenital heart defect characterized by malformation of the tricuspid valve and displacement of the valve leaflets into the right ventricle. It often presents with a wide spectrum of clinical manifestations, making diagnosis challenging. We present a unique case of Ebstein's anomaly where the diagnosis was unexpectedly made due to severe hemodynamic compromise. Case Presentation: A 27 - year - old male with a history of recurrent palpitations and dyspnea presented to the emergency department with sudden - onset chest pain and syncope. Initial evaluation revealed profound cyanosis and hypotension. Echocardiography demonstrated marked tricuspid regurgitation, right ventricular dilatation, and severe hemodynamic compromise. These findings prompted an urgent surgical consult. Management and Outcome: The patient underwent emergent surgical intervention, during which the diagnosis of Ebstein's anomaly was confirmed. Surgical repair involved tricuspid valve repair and right ventricular plication. Postoperatively, the patient's hemodynamics improved significantly, and he experienced a remarkable resolution of his symptoms. Ebstein's anomaly is a rare but potentially life - threatening congenital heart defect that can present in adulthood with severe hemodynamic compromise. Timely recognition and intervention are crucial for favorable outcomes. This case report underscores the importance of considering Ebstein's anomaly in the differential diagnosis of acute hemodynamic instability, especially in patients with a history of cardiac symptoms.
Keywords: Ebsteins anomaly, congenital heart disease, fractionated qrs
Edition: Volume 13 Issue 5, May 2024,
Pages: 1579 - 1581