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Case Studies | Obstetrics and Gynecology | India | Volume 13 Issue 7, July 2024 | Rating: 3.9 / 10
Leiomyoma in a Diagnosed Case of MRKH Syndrome: A Case Report
Nayila Khanam | Roshan Perween [2] | Seema Hakim [2]
Abstract: Introduction: Primary amenorrhea is the failure to reach menarche. The second most frequent cause of primary amenorrhea, after gonadal dysgenesis, is the Mayer - Rokitansky - K?ster - Hauser (MRKH) syndrome. Here, we present a rare instance of leiomyoma in a diagnosed case of MRKH syndrome. Case Report: A 35 - year - old woman presented to our Gynaecology OPD for abdominal pain and progressive abdominal distention for 8 months. Upon primary clinical assessment, she reported primary amenorrhea and primary infertility. There is no historical past illness. Her Physical Examination showed normal breast development and normal female body contour. Her external genitalia was normal. The patient was diagnosed with a case of MRKH. On USG bulky and heterogeneous uterus with a sub - endometrial cyst of myometrium suggestive of adenomyosis, endometrial hyperplasia, and posterior fundal wall fibroid mass 20 ? 13 cm on right adnexa up to gastric region showing low vascularity, uterine or broad ligament fibroid was found. Conclusion: Women with MRKH syndrome who present with abdominal pain and mass. Ultrasonography is the first imaging to evaluate the pelvic mass and genitourinary system. Magnetic resonance imaging is a more accurate modality to confirm the pelvic mass, and evaluate the genitourinary system and may give signs of malignant tendencies. Complete removal by laparoscopic is recommended to manage this case.
Keywords: MRKH syndrome, Leiomyoma, Primary amenorrhea
Edition: Volume 13 Issue 7, July 2024,
Pages: 223 - 225